Developmental Neuropathology
Chapter 10: Chiari Malformations
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Chiari malformations: first described by Hans Chiari in the late 19th century, it encompasses a series of hindbrain deformities associated with hydrocephalus.

Four types:

Chiari I malformations are not really herniation syndromes, although chronic herniation is sometimes called Chiari I. Pathology is distinct from herniation.

Chiari II malformations are also called Arnold-Chiari malformations, although the use of the name Arnold is not really correct.


Embryology and Genetics

Clinical features

Macroscopy and Histopathology

Differential diagnosis


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